In some cases, treatment may not be required.

Percutaneous balloon pulmonary dilation (valvuloplasty) has recently been found quite successful as treatment for the form of pulmonary valve stenosis which occurs without the presence of other heart defects.

Surgical repair of the defect (heart valve surgery) is usually performed when the child has reached pre-school age. Oxygen may be required prior to surgery if symptoms are severe.

Medications used before surgery may include prostaglandins (PGE) to maintain pulmonary blood flow, water pills to remove the excess fluid, anti-arrhythmics to improve the heart function, and blood thinners to prevent clots.

The outcome may be poor without surgical repair. The outcome is good with successful surgery.

• heart failure
• right ventricular hypertrophy (enlargement)

Call your health care provider if symptoms which may be associated with pulmonary valve stenosis occur.

Call your health care provider if swelling (of the ankles or any area), difficulty breathing, or other new symptoms develop in a person who has treated or untreated pulmonary valve stenosis.