Abdominal muscles
Abdominal muscles


Prune belly syndrome

Alternative Names:
Eagle-Barrett syndrome

Treatment:
Treatment requires surgical intervention to maintain drainage of the renal system and protect remaining renal function. Typical surgeries might include:
  • pyelostomy (an opening into the kidney; usually with placement of a drainage tube)
  • vesicostomy (an opening into the bladder; usually with placement of a drainage tube)
  • reconstructive surgery
  • prenatal surgery to correct posterior urethral valves that don't open is likely to become more widely available in the future
Other treatment:

Expectations (prognosis):
The outlook is poor to fair. About one third of affected infants die early or are still born. Infants that survive may have life-long urinary tract or other problems.

Complications:


Calling your health care provider:
This diagnosis used to only be made in the hospital at the time of birth. If you have a child with diagnosed prune belly syndrome, call your health care provider at the first sign of a urinary tract infection or other urinary symptoms. If your child is diagnosed with distended bladder or enlarged kidneys on prenatal ultrasound seek prompt consultation with a specialist in high-risk obstetrics or a perinatologist.


Review Date: 12/3/2001
Reviewed By: David G. Brooks, M.D., Ph.D., Division of Medical Genetics, University of Pennsylvania Medical Center, Philadelphia, PA. Review provided by VeriMed Healthcare Network.

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